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Table 2 Conditions associated with systemic fibrosis

From: Hyper-IgG4 disease: report and characterisation of a new disease

Name

Synonyms

 

RPF

Ormond's disease

Systemic[109,111,113,135], lung[32,32,53,115,136,136,137], liver[138], breast, pancreas[5,139-141],

Retro-orbital tumour

Fibrous pseudotumour of the orbit, Graves' orbitopathy

RPF[124,129-131,142-145]

Riedel's thyroiditis

 

RPF[132,133,146-148] MFF[127,128,147,149,150]

Chronic sclerosing sialadenitis[151]

Kuttner's tumour

 

Panniculitis

Weber-Christian syndrome steatonecrosis, necrosing panniculitis

Systemic[110], RPF[135,152-155] Biliary cirrhosis[156], pancreas[157]

Sclerosing pancreatitis[158]

Primary inflammatory pancreatitis (P)[159], lymphoplasmacytic sclerosing P[7,160,161], autoimmune P[162], sclerosing pancreaticocholangitis[163], pancreatic pseudo-tumour[95]

RPF[5,97,139,161,164,165], cholangitis[95,160,164,166,167], systemic[83,168-171] gastric ulcer[172], lung[173,174] panniculitis[157], mesentery[175]

Sclerosing cholangitis

 

MFF[128], pancreas[92,166]

Bronchiolitis obliterans with organizing pneumonia

Cryptogenic organizing pneumonia, pulmonary hyalinizing granuloma.

Systemic[50,176], pancreas[173,174], liver[177], RPF[115,136,137], renal[46,136], mediastinum[178,179]

Benign pleural mesothelioma[180,181], calcifying pseudotumour[182,183]

Asbestos-related?

RPF[11,26-28,32,32] peritoneum[56,184,185] pleura[54,55,186]

  1. RPF, retroperitoneal fibrosis; MFF, multifocal fibrosclerosis