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Table 3 Rare associations with IgG4-related conditions (Case reports)

From: Hyper-IgG4 disease: report and characterisation of a new disease

Head and neck
Submandibular gland fibrosis Pancreas[95], cholangitis[187,188], pseudotumour[189]
Parotid involvement pancreas[171]
Sjögren's syndrome Pancreas[171,190], RPF[164], BOOP[191]
Maculopathy MFF[126]
Uveitis RPF[192]
Conjunctiva Pseudotumour[86]
Hashimoto's disease, Graves' disease RPF[193]
Cardiovascular
Constrictive pericarditis RPF[194]
Heart valves RPF[20,22]
Mediastinal fibrosis RPF[194-196]
Chronic periaortitis/aneurysm RPF[197-205]
Vasculitis RPF[125,206,207]
Occlusive phlebitis MFF[149]
Intermittent claudication RPF[208]
Rheumatology
Rheumatoid arthritis BOOP[176], RPF[209]
Polymyalgia rheumatica BOOP[210]
Ankylosing spondylitis RPF[211]
Periarticular fibrosis RPF[212]
Skeletal hyperostosis RPF[213]
Dermatomyositis Pseudotumour[88], BOOP[214]
Polymyositis BOOP[191,215]
Scleroderma RPF[216]
Other autoimmune conditions
Systemic lupus erythematosus RPF[217]
Idiopathic thrombocytopenic purpura RPF[218,219]
Haemolytic anaemia Lung[220], cholangitis[221]
Central nervous system
Brain PCG[107], xanthogranuloma[118,222]
Sella MFF[124,126]
Spinal cord compression RPF[223]
Gastrointestinal
Primary biliary cirrhosis RPF[224], BOOP[176]
Mesentery RPF[112,152,175,225], pseudotumour[102,153,155]
Bladder/pelvic mass RPF[49,208,226,227]
Duodenal obstruction RPF[228,229]
Portal hypertension RPF[230]
Others
Familial multifocal fibrosclerosis Familial RPF MFF[43] RPF[42]
Proliferative crescentic glomerulonephritis, membranous glomerulonephritis RPF[231] RPF[232]
Interstitial nephritis Pancreas[233]
Testicular involvement RPF[126,234]
  1. MFF, multifocal fibrosclerosis; RPF, retroperitoneal fibrosis; BOOP, bronchiolitis obliterans with organizing pneumonia; PCG, plasma-cell granuloma.