Figure 2

Coronal reformatted contrast enhanced computed tomography images of patient #1, obtained at the time of the diagnosis (A) and 4.5 years after the diagnosis (B). The latter reveals severe hydronephrosis and marked cortical thinning of the left kidney and a peri-renal mass compressing the right kidney. Also, note the fine bilateral peri-renal infiltrate forming a `hairy kidney’ appearance.