From: Interstitial lung diseases in the hospitalized patient
Classification | Clinical-radiological-pathological diagnosis | Histopathologic pattern |
---|---|---|
ILDs of known cause | Environmental or drug related | Depends on underlying disease |
Connective tissue disease related | Depends on underlying disease | |
Hypersensitivity pneumonitis | ||
Idiopathic interstitial pneumonias (IIPs) | ||
Major IIPs | ||
Chronic fibrosing IPs | IPF | UIP |
Idiopathic NSIP | NSIP | |
Smoking-related IPs | DIP | DIP |
RB-ILD | Respiratory bronchiolitis | |
Acute/subacute IPs | COP | Organizing pneumonia |
AIP | Diffuse alveolar damage | |
Rare IIPs | Idiopathic LIP | LIP |
Idiopathic PPFE | Elastotic fibrosis of pleura and subpleural parenchyma | |
Unclassifiable IIPs | ||
Granulomatous lung disorders | Sarcoidosis | Non-necrotizing granuloma |
Other forms of ILD | LAM | Cysts and proliferation of LAM cells |
PLCH | Proliferation of Langerhans cells | |
Eosinophilic pneumonia | Depends on disease onset |