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Table 1 Prevalence of MEN1 manifestations

From: MEN1 redefined, a clinical comparison of mutation-positive and mutation-negative patients

MEN1 manifestations

Total

Mutation-positive

Mutation-negative

n (%)

n (%)

n (%)

Number of patients

322

292

30

Primary hyperparathyroidism

280 (87.0)

252 (86.0)

28 (93.3)

Duodenopancreatic neuroendocrine tumors

180 (55.9)

173 (59.2)

7 (23.3)

Pituitary tumor

141 (49.6)

116 (39.7)

25 (83.3)

Lung neuroendocrine tumor

62 (19.3)

62 (21.2)

0

Thymic neuroendocrine tumor

13 (4.0)

13 (4.5)

0

Gastric neuroendocrine tumor

12 (3.7)

12 (4.1)

0

Adrenal tumor

101 (31.4)

100 (34.1)

1 (3.3)